VERTICAL PDA STENTING IN PULMONARY ATRESIA WITH INTACT INTERVENTRICULAR SEPTUM

Abstract

Pulmonary atresia with intact interventricular septum(PA-IVS) is a rare congenital
lesion. PA-IVS involves complete blockage of the pulmonary valve located on the
right side of the heart. This blockage thus prevents the flow of blood to the lungs.
Because of this lack of blood flowing through the right side of the heart, the
structures on that side, such as the pulmonary valve and the tricuspid valve, may
be abnormally small. The genetic cause of PA-IVS is unknown. We report a 6-
month-old infant with congenital heart disease including; pulmonary atresia,
intact ventricular septum, right ventricular hypoplasia, and vertical persistant
ductus arteriosus (PDA) arising from left subclavian artery with stenosis at
pulmonary end. PDA stenting was performed with successful hemodynamic
after procedure.